Survival statistics, estimated using data from national cystic fibrosis (CF) registries, inform the CF community and monitor disease progression. Thi…
Pulmonary exacerbations are associated with increased morbidity and mortality in people with cystic fibrosis (CF). There is no consensus about which…
The aims of the study were to investigate family and hospital staff views about the use of spring-infusor devices for administration of intravenous a…
Macrophages are the major resident immune cells in human airways coordinating responses to infection and injury. In cystic fibrosis, neutrophils are…
Promising results from an Australian-led clinical trial could drastically change the way we care for young children with cystic fibrosis (CF).
Infants with cystic fibrosis (CF) develop structural lung disease early in life, and viral infections are associated with progressive lung disease. W…
Primary ciliary dyskinesia (PCD) is a rare, progressive, inherited ciliopathic disorder, which is incurable and frequently complicated by the develop…
Diagnosis of chronic disease in a child can result in unresolved grief (UG) in parents. This study aimed to evaluate the efficacy of psychological in…
Cystic fibrosis (CF), due to pathogenic variants in CFTR gene, is associated with chronic infection/inflammation responsible for airway epithelium al…